Rowe, D W

Diminished type I collagen synthesis and reduced alpha 1(I) collagen messenger RNA in cultured fibroblasts from patients with dominantly inherited (type I) osteogenesis imperfecta. [electronic resource] - The Journal of clinical investigation Aug 1985 - 604-11 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.

0021-9738

10.1172/JCI112012 doi


Adult
Collagen--biosynthesis
Electrophoresis, Polyacrylamide Gel
Fibroblasts--metabolism
Fluorometry
Humans
Male
Nucleic Acid Hybridization
Osteogenesis Imperfecta--genetics
Pedigree
RNA, Messenger--metabolism