Manabe, S Hereditary tyrosinemia. Formation of succinylacetone-amino acid adducts. [electronic resource] - The Journal of experimental medicine Sep 1985 - 1060-74 p. digital Publication Type: Journal Article; Research Support, U.S. Gov't, P.H.S. ISSN: 0022-1007 Standard No.: 10.1084/jem.162.3.1060 doi Subjects--Topical Terms: Amino Acid Metabolism, Inborn Errors--urineAmino Acids--metabolismChromatography, High Pressure LiquidChromatography, Thin LayerGlutathione--metabolismHeptanoates--pharmacologyHeptanoic Acids--urineHumansHydrogen-Ion ConcentrationHydrolases--deficiencyLysine--metabolismPorphobilinogen Synthase--antagonists & inhibitorsSpectrophotometry, UltravioletTyrosine--blood