Manabe, S

Hereditary tyrosinemia. Formation of succinylacetone-amino acid adducts. [electronic resource] - The Journal of experimental medicine Sep 1985 - 1060-74 p. digital

Publication Type: Journal Article; Research Support, U.S. Gov't, P.H.S.

0022-1007

10.1084/jem.162.3.1060 doi


Amino Acid Metabolism, Inborn Errors--urine
Amino Acids--metabolism
Chromatography, High Pressure Liquid
Chromatography, Thin Layer
Glutathione--metabolism
Heptanoates--pharmacology
Heptanoic Acids--urine
Humans
Hydrogen-Ion Concentration
Hydrolases--deficiency
Lysine--metabolism
Porphobilinogen Synthase--antagonists & inhibitors
Spectrophotometry, Ultraviolet
Tyrosine--blood