Dawson, G

Apparent cathepsin B deficiency in neuronal ceroid lipofuscinosis can be explained by peroxide inhibition. [electronic resource] - Biochemical and biophysical research communications Aug 1987 - 267-74 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.

0006-291X

10.1016/s0006-291x(87)80116-x doi


Cathepsin B--metabolism
Fibroblasts--enzymology
Hexosaminidases--metabolism
Humans
Hydrogen Peroxide--pharmacology
Lipid Peroxides--metabolism
Lysosomes--enzymology
Neuronal Ceroid-Lipofuscinoses--enzymology