Dawson, G
Abnormal cathepsin B activity in Batten disease. [electronic resource]
- American journal of medical genetics. Supplement 1988
- 209-20 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.
1040-3787
10.1002/ajmg.1320310624 doi
Acid Phosphatase--metabolism
Arachidonic Acid
Arachidonic Acids--metabolism
Cathepsin B--metabolism
Cells, Cultured
Child
Child, Preschool
Cysteine Endopeptidases--metabolism
Fibroblasts--enzymology
Humans
Hydrogen Peroxide--pharmacology
Hydrolases--metabolism
Kinetics
Lysosomes--enzymology
Neuronal Ceroid-Lipofuscinoses--enzymology
Skin--enzymology