García-Puga, Mikel

Myotonic Dystrophy type 1 cells display impaired metabolism and mitochondrial dysfunction that are reversed by metformin. [electronic resource] - Aging 04 2020 - 6260-6275 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1945-4589

10.18632/aging.103022 doi


Adult
Aged
Energy Metabolism--drug effects
Female
Fibroblasts--metabolism
Humans
Hypoglycemic Agents--administration & dosage
Leukocytes, Mononuclear--metabolism
Male
Metformin--administration & dosage
Mitochondria--metabolism
Mitochondrial Diseases--drug therapy
Myotonic Dystrophy--blood
Oxidative Phosphorylation--drug effects
Oxygen Consumption--drug effects
Reactive Oxygen Species--analysis
Treatment Outcome