Fernández, Gabriela

Myofibers deficient in connexins 43 and 45 expression protect mice from skeletal muscle and systemic dysfunction promoted by a dysferlin mutation. [electronic resource] - Biochimica et biophysica acta. Molecular basis of disease 08 2020 - 165800 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1879-260X

10.1016/j.bbadis.2020.165800 doi


Animals
Calcium--metabolism
Connexin 43--deficiency
Connexins--deficiency
Creatine Kinase--blood
Disease Models, Animal
Dysferlin--deficiency
Gene Expression
Humans
Male
Mice
Mice, Inbred C57BL
Mice, Knockout
Muscular Dystrophies, Limb-Girdle--genetics
Mutation
Myofibrils--genetics
Permeability
Physical Conditioning, Animal
Rotarod Performance Test
Sarcolemma--metabolism