Zhang, Xu

Structure-function analyses of the G729R 2-oxoadipate dehydrogenase genetic variant associated with a disorder of l-lysine metabolism. [electronic resource] - The Journal of biological chemistry 06 2020 - 8078-8095 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, Non-P.H.S.

1083-351X

10.1074/jbc.RA120.012761 doi


Fibroblasts--chemistry
Genetic Variation--genetics
Humans
Ketoglutarate Dehydrogenase Complex
Ketone Oxidoreductases--chemistry
Kinetics
Lysine--chemistry
Models, Molecular
Molecular Structure
Structure-Activity Relationship