Inui, K

Hexosaminidase A activity in skin fibroblasts from various types of GM2 gangliosidosis using a fluorogenic sulphated substrate. [electronic resource] - Journal of inherited metabolic disease 1985 - 149-50 p. digital

Publication Type: Journal Article

0141-8955

10.1007/BF01819302 doi


Catalysis
Cell Line
Fibroblasts--enzymology
G(M2) Ganglioside--metabolism
Gangliosidoses--enzymology
Hexosaminidase A
Humans
Hymecromone--analogs & derivatives
Skin--enzymology
beta-N-Acetylhexosaminidases--metabolism