TY - GEN AU - Jones,Frances E AU - Murray,Lydia S AU - McNeilly,Sarah AU - Dean,Afshan AU - Aman,Alisha AU - Lu,Yinhui AU - Nikolova,Nija AU - Malomgré,Ruben AU - Horsburgh,Karen AU - Holmes,William M AU - Kadler,Karl E AU - Van Agtmael,Tom TI - 4-Sodium phenyl butyric acid has both efficacy and counter-indicative effects in the treatment of Col4a1 disease SN - 1460-2083 PY - 2019///0621 KW - Animals KW - Basement Membrane KW - drug effects KW - Cerebral Hemorrhage KW - drug therapy KW - Collagen Type IV KW - genetics KW - Disease Models, Animal KW - Endoplasmic Reticulum Stress KW - Humans KW - Mice KW - Molecular Targeted Therapy KW - Mutation KW - Phenylbutyrates KW - administration & dosage N1 - Publication Type: Journal Article; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1093/hmg/ddy369 ER -