Onojafe, Ighovie F

Minimal Efficacy of Nitisinone Treatment in a Novel Mouse Model of Oculocutaneous Albinism, Type 3. [electronic resource] - Investigative ophthalmology & visual science 10 2018 - 4945-4952 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Intramural

1552-5783

10.1167/iovs.16-20293 doi


Administration, Oral
Albinism, Oculocutaneous--blood
Animals
Blotting, Western
Cyclohexanones--therapeutic use
Disease Models, Animal
Enzyme Inhibitors--therapeutic use
Genotyping Techniques
Melanins--metabolism
Melanosomes--pathology
Membrane Glycoproteins--genetics
Mice
Mice, Inbred BALB C
Mice, Inbred C57BL
Mice, Inbred DBA
Microscopy, Electron, Transmission
Nitrobenzoates--therapeutic use
Oxidoreductases--genetics
Real-Time Polymerase Chain Reaction
Treatment Outcome
Tyrosine--blood