TY  - GEN
AU  - Jiang,Xu
AU  - Fang,Guodong
AU  - Dong,Li
AU  - Jin,Peifeng
AU  - Ding,Lu
AU  - Zhang,Haizeng
AU  - Fan,Junming
AU  - Mao,Sunzhong
AU  - Fan,Xiaofang
AU  - Gong,Yongsheng
AU  - Wang,Yongyu
TI  - Chemical chaperone 4-phenylbutyric acid alleviates the aggregation of human familial pulmonary fibrosis-related mutant SP-A2 protein in part through effects on GRP78
SN  - 1879-260X
PY  - 2019///0520
KW  - A549 Cells
KW  - Animals
KW  - CHO Cells
KW  - Cricetulus
KW  - Dose-Response Relationship, Drug
KW  - Endoplasmic Reticulum Chaperone BiP
KW  - Heat-Shock Proteins
KW  - metabolism
KW  - Humans
KW  - Leupeptins
KW  - pharmacology
KW  - Mutation
KW  - Phenylbutyrates
KW  - Protein Aggregates
KW  - drug effects
KW  - Pulmonary Fibrosis
KW  - genetics
KW  - Pulmonary Surfactant-Associated Protein A
N1  - Publication Type: Journal Article; Research Support, Non-U.S. Gov't
UR  - https://doi.org/10.1016/j.bbadis.2018.08.014
ER  -