Waskowicz, Lauren R

Bezafibrate induces autophagy and improves hepatic lipid metabolism in glycogen storage disease type Ia. [electronic resource] - Human molecular genetics 01 2019 - 143-154 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1460-2083

10.1093/hmg/ddy343 doi


Animals
Autophagy--drug effects
Bezafibrate--metabolism
Disease Models, Animal
Dogs
Glucose--metabolism
Glucose-6-Phosphatase--metabolism
Glucose-6-Phosphate--metabolism
Glycogen--metabolism
Glycogen Storage Disease Type I--drug therapy
Lipid Metabolism--drug effects
Liver--drug effects
Mice
Mice, Knockout
Triglycerides--metabolism