TY  - GEN
AU  - Chatzispyrou,Iliana A
AU  - Guerrero-Castillo,Sergio
AU  - Held,Ntsiki M
AU  - Ruiter,Jos P N
AU  - Denis,Simone W
AU  - IJlst,Lodewijk
AU  - Wanders,Ronald J
AU  - van Weeghel,Michel
AU  - Ferdinandusse,Sacha
AU  - Vaz,Frédéric M
AU  - Brandt,Ulrich
AU  - Houtkooper,Riekelt H
TI  - Barth syndrome cells display widespread remodeling of mitochondrial complexes without affecting metabolic flux distribution
SN  - 1879-260X
PY  - 2018///1211
KW  - Acyltransferases
KW  - Barth Syndrome
KW  - genetics
KW  - Cardiolipins
KW  - metabolism
KW  - Case-Control Studies
KW  - Fibroblasts
KW  - Healthy Volunteers
KW  - Humans
KW  - Metabolic Networks and Pathways
KW  - Metabolomics
KW  - Mitochondria
KW  - Mitochondrial Membranes
KW  - Mutation
KW  - Oxidative Phosphorylation
KW  - Primary Cell Culture
KW  - Proteomics
KW  - Signal Transduction
KW  - Skin
KW  - cytology
KW  - Transcription Factors
N1  - Publication Type: Journal Article; Research Support, Non-U.S. Gov't
UR  - https://doi.org/10.1016/j.bbadis.2018.08.041
ER  -