A severe mouse model of spinal muscular atrophy develops early systemic inflammation. [electronic resource]
- Human molecular genetics 12 2018
- 4061-4076 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
1460-2083
10.1093/hmg/ddy300 doi
Animals Central Nervous System--metabolism Cytokines--genetics Disease Models, Animal Flow Cytometry Gene Expression Regulation--genetics Humans Inflammation--chemically induced Lipopolysaccharides--toxicity Mice Mice, Transgenic Muscle, Skeletal--metabolism Muscular Atrophy, Spinal--genetics Spinal Cord--metabolism Survival of Motor Neuron 1 Protein--genetics Survival of Motor Neuron 2 Protein--genetics Tumor Suppressor Proteins--genetics