TY  - GEN
AU  - Chan,Wing Lee
AU  - Steiner,Magdalena
AU  - Witkos,Tomasz
AU  - Egerer,Johannes
AU  - Busse,Björn
AU  - Mizumoto,Shuji
AU  - Pestka,Jan M
AU  - Zhang,Haikuo
AU  - Hausser,Ingrid
AU  - Khayal,Layal Abo
AU  - Ott,Claus-Eric
AU  - Kolanczyk,Mateusz
AU  - Willie,Bettina
AU  - Schinke,Thorsten
AU  - Paganini,Chiara
AU  - Rossi,Antonio
AU  - Sugahara,Kazuyuki
AU  - Amling,Michael
AU  - Knaus,Petra
AU  - Chan,Danny
AU  - Lowe,Martin
AU  - Mundlos,Stefan
AU  - Kornak,Uwe
TI  - Impaired proteoglycan glycosylation, elevated TGF-β signaling, and abnormal osteoblast differentiation as the basis for bone fragility in a mouse model for gerodermia osteodysplastica
SN  - 1553-7404
PY  - 2018///0710
KW  - Animals
KW  - Bone Diseases
KW  - congenital
KW  - Cell Differentiation
KW  - Decorin
KW  - metabolism
KW  - Dermatan Sulfate
KW  - Disease Models, Animal
KW  - Dwarfism
KW  - Female
KW  - Fractures, Bone
KW  - genetics
KW  - Glycosylation
KW  - Golgi Matrix Proteins
KW  - Mesenchymal Stem Cells
KW  - pathology
KW  - Mice, Inbred C57BL
KW  - Mice, Transgenic
KW  - Osteoblasts
KW  - Proteoglycans
KW  - Signal Transduction
KW  - Skin Diseases, Genetic
KW  - Transforming Growth Factor beta
KW  - Vesicular Transport Proteins
N1  - Publication Type: Journal Article; Research Support, Non-U.S. Gov't
UR  - https://doi.org/10.1371/journal.pgen.1007242
ER  -