Chan, Wing Lee <br/><br/>
Impaired proteoglycan glycosylation, elevated TGF-β signaling, and abnormal osteoblast differentiation as the basis for bone fragility in a mouse model for gerodermia osteodysplastica.  [electronic resource] 

 -  PLoS genetics  03 2018 
 - e1007242 p.  digital 
<br/><br/> Publication Type: Journal Article; Research Support, Non-U.S. Gov't 
<br/><br/><label>ISSN: </label>1553-7404 
<br/><br/><label>Standard No.: </label>10.1371/journal.pgen.1007242  doi 
<br/><br/><label>Subjects--Topical Terms: </label><br/>Animals<br/>Bone Diseases--congenital<br/>Cell Differentiation<br/>Decorin--metabolism<br/>Dermatan Sulfate--metabolism<br/>Disease Models, Animal<br/>Dwarfism--metabolism<br/>Female<br/>Fractures, Bone--genetics<br/>Glycosylation<br/>Golgi Matrix Proteins<br/>Mesenchymal Stem Cells--pathology<br/>Mice, Inbred C57BL<br/>Mice, Transgenic<br/>Osteoblasts--metabolism<br/>Proteoglycans--metabolism<br/>Signal Transduction<br/>Skin Diseases, Genetic--metabolism<br/>Transforming Growth Factor beta--metabolism<br/>Vesicular Transport Proteins--genetics