Cathepsin B inhibition attenuates cardiovascular pathology in mucopolysaccharidosis I mice. [electronic resource]
- Life sciences Mar 2018
- 102-109 p. digital
Publication Type: Journal Article
1879-0631
10.1016/j.lfs.2018.01.020 doi
Animals Aorta--pathology Cardiovascular System--diagnostic imaging Cathepsin B--antagonists & inhibitors Collagenases--metabolism Cysteine Proteinase Inhibitors--therapeutic use Dipeptides--therapeutic use Female Fibroblasts--metabolism Heart Function Tests Heart Valve Diseases--diagnostic imaging Humans Lysosomes--metabolism Male Mice Mice, Inbred C57BL Mucopolysaccharidosis I--diagnostic imaging Pancreatic Elastase--metabolism