Gonzalez, Esteban Alberto

Cathepsin B inhibition attenuates cardiovascular pathology in mucopolysaccharidosis I mice. [electronic resource] - Life sciences Mar 2018 - 102-109 p. digital

Publication Type: Journal Article

1879-0631

10.1016/j.lfs.2018.01.020 doi


Animals
Aorta--pathology
Cardiovascular System--diagnostic imaging
Cathepsin B--antagonists & inhibitors
Collagenases--metabolism
Cysteine Proteinase Inhibitors--therapeutic use
Dipeptides--therapeutic use
Female
Fibroblasts--metabolism
Heart Function Tests
Heart Valve Diseases--diagnostic imaging
Humans
Lysosomes--metabolism
Male
Mice
Mice, Inbred C57BL
Mucopolysaccharidosis I--diagnostic imaging
Pancreatic Elastase--metabolism