TY - GEN AU - Calo,Eliezer AU - Gu,Bo AU - Bowen,Margot E AU - Aryan,Fardin AU - Zalc,Antoine AU - Liang,Jialiang AU - Flynn,Ryan A AU - Swigut,Tomek AU - Chang,Howard Y AU - Attardi,Laura D AU - Wysocka,Joanna TI - Tissue-selective effects of nucleolar stress and rDNA damage in developmental disorders SN - 1476-4687 PY - 2018///0522 KW - Animals KW - Apoptosis KW - Benzothiazoles KW - pharmacology KW - Cell Nucleolus KW - drug effects KW - Cell Nucleus KW - Chromatin KW - metabolism KW - DEAD-box RNA Helicases KW - deficiency KW - DNA Damage KW - DNA, Ribosomal KW - genetics KW - DNA-Directed RNA Polymerases KW - Embryonic Stem Cells KW - cytology KW - HeLa Cells KW - Humans KW - Intracellular Signaling Peptides and Proteins KW - Mandibulofacial Dysostosis KW - embryology KW - Mice KW - Naphthyridines KW - Neural Crest KW - enzymology KW - Nuclear Proteins KW - Organ Specificity KW - Phenotype KW - Phosphoproteins KW - Protein Transport KW - RNA Helicases KW - RNA Polymerase I KW - antagonists & inhibitors KW - RNA, Ribosomal KW - biosynthesis KW - Ribosomal Proteins KW - Ribosomes KW - Skull KW - pathology KW - Stress, Physiological KW - Tumor Suppressor Protein p53 KW - Xenopus KW - Zebrafish KW - Zebrafish Proteins N1 - Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1038/nature25449 ER -