CORK Study in Cystic Fibrosis: Sustained Improvements in Ultra-Low-Dose Chest CT Scores After CFTR Modulation With Ivacaftor. [electronic resource]
- Chest 02 2018
- 395-403 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
1931-3543
10.1016/j.chest.2017.10.005 doi
Adolescent Adult Aminophenols--therapeutic use Chloride Channel Agonists--therapeutic use Cystic Fibrosis--diagnostic imaging Cystic Fibrosis Transmembrane Conductance Regulator--genetics Female Forced Expiratory Volume--physiology Humans Male Prospective Studies Quinolones--therapeutic use Radiography, Thoracic--methods Saliva--microbiology Tomography, X-Ray Computed--methods Young Adult