Rademacher, Sebastian

Metalloprotease-mediated cleavage of PlexinD1 and its sequestration to actin rods in the motoneuron disease spinal muscular atrophy (SMA). [electronic resource] - Human molecular genetics 10 2017 - 3946-3959 p. digital

Publication Type: Journal Article

1460-2083

10.1093/hmg/ddx282 doi


Actin Cytoskeleton--metabolism
Animals
Axons--metabolism
Cell Adhesion Molecules, Neuronal--metabolism
Cell Differentiation--physiology
Cytoskeleton--metabolism
Disease Models, Animal
Humans
Intracellular Signaling Peptides and Proteins
Membrane Glycoproteins--metabolism
Metalloproteases--metabolism
Mice
Motor Neurons--metabolism
Muscular Atrophy, Spinal--metabolism
Nerve Tissue Proteins--metabolism
Spinal Cord--metabolism
Survival of Motor Neuron 1 Protein--metabolism