Metalloprotease-mediated cleavage of PlexinD1 and its sequestration to actin rods in the motoneuron disease spinal muscular atrophy (SMA). [electronic resource]
- Human molecular genetics 10 2017
- 3946-3959 p. digital
Publication Type: Journal Article
1460-2083
10.1093/hmg/ddx282 doi
Actin Cytoskeleton--metabolism Animals Axons--metabolism Cell Adhesion Molecules, Neuronal--metabolism Cell Differentiation--physiology Cytoskeleton--metabolism Disease Models, Animal Humans Intracellular Signaling Peptides and Proteins Membrane Glycoproteins--metabolism Metalloproteases--metabolism Mice Motor Neurons--metabolism Muscular Atrophy, Spinal--metabolism Nerve Tissue Proteins--metabolism Spinal Cord--metabolism Survival of Motor Neuron 1 Protein--metabolism