Farah, Benjamin L

Renal endoplasmic reticulum stress is coupled to impaired autophagy in a mouse model of GSD Ia. [electronic resource] - Molecular genetics and metabolism 11 2017 - 95-98 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1096-7206

10.1016/j.ymgme.2017.08.013 doi


Animals
Autophagy--drug effects
Disease Models, Animal
Down-Regulation
Endoplasmic Reticulum Stress--drug effects
Glucose-6-Phosphatase--metabolism
Glucose-6-Phosphate--metabolism
Glycogen Storage Disease Type I--complications
Immunosuppressive Agents--pharmacology
Kidney--pathology
Mice
Sirolimus--pharmacology