Ramirez, Francesco

Marfan syndrome; A connective tissue disease at the crossroads of mechanotransduction, TGFβ signaling and cell stemness. [electronic resource] - Matrix biology : journal of the International Society for Matrix Biology 10 2018 - 82-89 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Review

1569-1802

10.1016/j.matbio.2017.07.004 doi


Animals
Disease Models, Animal
Fibrillin-1--genetics
Humans
Marfan Syndrome--genetics
Mechanotransduction, Cellular
Mutation
Myocardium--metabolism
Signal Transduction
Stem Cells--metabolism
Transforming Growth Factor beta--metabolism