TY - GEN AU - Piret,Sian E AU - Olinger,Eric AU - Reed,Anita A C AU - Nesbit,M Andrew AU - Hough,Tertius A AU - Bentley,Liz AU - Devuyst,Olivier AU - Cox,Roger D AU - Thakker,Rajesh V TI - A mouse model for inherited renal fibrosis associated with endoplasmic reticulum stress SN - 1754-8411 PY - 2018///0323 KW - Animals KW - Disease Models, Animal KW - Endoplasmic Reticulum Chaperone BiP KW - Endoplasmic Reticulum Stress KW - Fibrosis KW - Germ Cells KW - metabolism KW - Inflammation KW - pathology KW - Inheritance Patterns KW - genetics KW - Kidney KW - Kidney Diseases KW - blood KW - Mice KW - Mutation KW - Transcription Factor CHOP KW - Unfolded Protein Response KW - Up-Regulation KW - Uromodulin N1 - Publication Type: Journal Article UR - https://doi.org/10.1242/dmm.029488 ER -