TY - GEN AU - Huang,Yan AU - Powers,Corey AU - Moore,Victoria AU - Schafer,Caitlin AU - Ren,Mindong AU - Phoon,Colin K L AU - James,Jeanne F AU - Glukhov,Alexander V AU - Javadov,Sabzali AU - Vaz,Frédéric M AU - Jefferies,John L AU - Strauss,Arnold W AU - Khuchua,Zaza TI - The PPAR pan-agonist bezafibrate ameliorates cardiomyopathy in a mouse model of Barth syndrome SN - 1750-1172 PY - 2018///0228 KW - Animals KW - Barth Syndrome KW - drug therapy KW - Bezafibrate KW - therapeutic use KW - Blotting, Western KW - Cardiolipins KW - metabolism KW - Cardiomyopathies KW - Disease Models, Animal KW - Echocardiography KW - Female KW - Male KW - Mice KW - Peroxisome Proliferator-Activated Receptors KW - agonists KW - Polymerase Chain Reaction N1 - Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1186/s13023-017-0605-5 ER -