Ferrari, Eleonora

Cysteamine re-establishes the clearance of Pseudomonas aeruginosa by macrophages bearing the cystic fibrosis-relevant F508del-CFTR mutation. [electronic resource] - Cell death & disease 01 2017 - e2544 p. digital

Publication Type: Journal Article

2041-4889

10.1038/cddis.2016.476 doi


Animals
Beclin-1--biosynthesis
Bone Marrow Cells--metabolism
Cysteamine--administration & dosage
Cystic Fibrosis--drug therapy
Cystic Fibrosis Transmembrane Conductance Regulator--genetics
Gene Expression Regulation--drug effects
Humans
Inflammation--drug therapy
Lung--metabolism
Macrophages--drug effects
Mice
Mice, Transgenic
Pseudomonas Infections--drug therapy
Pseudomonas aeruginosa--drug effects