Steffen, Janos Rapid degradation of mutant SLC25A46 by the ubiquitin-proteasome system results in MFN1/2-mediated hyperfusion of mitochondria. [electronic resource] - Molecular biology of the cell Mar 2017 - 600-612 p. digital Publication Type: Journal Article ISSN: 1939-4586 Standard No.: 10.1091/mbc.E16-07-0545 doi Subjects--Topical Terms: Apoptosis--physiologyAutophagy--physiologyGTP Phosphohydrolases--metabolismHEK293 CellsHeLa CellsHumansMitochondria--metabolismMitochondrial Dynamics--physiologyMitochondrial Membrane Transport Proteins--metabolismMitochondrial Membranes--metabolismMitochondrial Proteins--metabolismPhosphate Transport Proteins--metabolismProteasome Endopeptidase Complex--metabolismProteolysisUbiquitin--metabolismUbiquitin-Protein Ligases--metabolismUbiquitination