Le, Nhat T T

Motor neuron disease, TDP-43 pathology, and memory deficits in mice expressing ALS-FTD-linked UBQLN2 mutations. [electronic resource] - Proceedings of the National Academy of Sciences of the United States of America 11 2016 - E7580-E7589 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1091-6490

10.1073/pnas.1608432113 doi


Adaptor Proteins, Signal Transducing
Adaptor Proteins, Vesicular Transport--genetics
Amyotrophic Lateral Sclerosis--complications
Animals
Autophagy-Related Proteins
Cell Nucleus--metabolism
Cytoplasm--metabolism
DNA-Binding Proteins--metabolism
Disease Models, Animal
Frontotemporal Dementia--etiology
Humans
Inclusion Bodies--metabolism
Mice
Motor Neurons--metabolism
Mutation, Missense
Ubiquitination