TY - GEN AU - Ayers,Jacob I AU - Diamond,Jeffrey AU - Sari,Adriana AU - Fromholt,Susan AU - Galaleldeen,Ahmad AU - Ostrow,Lyle W AU - Glass,Jonathan D AU - Hart,P John AU - Borchelt,David R TI - Distinct conformers of transmissible misfolded SOD1 distinguish human SOD1-FALS from other forms of familial and sporadic ALS SN - 1432-0533 PY - 2017///0920 KW - Amyloid KW - genetics KW - Amyotrophic Lateral Sclerosis KW - diagnosis KW - Analysis of Variance KW - Animals KW - Bacterial Proteins KW - Disease Models, Animal KW - Humans KW - In Vitro Techniques KW - Luminescent Proteins KW - Mice KW - Mice, Transgenic KW - Microscopy, Electron KW - Mutation KW - Organ Culture Techniques KW - Protein Folding KW - Proteostasis Deficiencies KW - Spinal Cord KW - metabolism KW - Superoxide Dismutase-1 N1 - Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1007/s00401-016-1623-4 ER -