Ayers, Jacob I

Distinct conformers of transmissible misfolded SOD1 distinguish human SOD1-FALS from other forms of familial and sporadic ALS. [electronic resource] - Acta neuropathologica 12 2016 - 827-840 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1432-0533

10.1007/s00401-016-1623-4 doi


Amyloid--genetics
Amyotrophic Lateral Sclerosis--diagnosis
Analysis of Variance
Animals
Bacterial Proteins--genetics
Disease Models, Animal
Humans
In Vitro Techniques
Luminescent Proteins--genetics
Mice
Mice, Transgenic
Microscopy, Electron
Mutation--genetics
Organ Culture Techniques
Protein Folding
Proteostasis Deficiencies--diagnosis
Spinal Cord--metabolism
Superoxide Dismutase-1--genetics