Distinct conformers of transmissible misfolded SOD1 distinguish human SOD1-FALS from other forms of familial and sporadic ALS. [electronic resource]
- Acta neuropathologica 12 2016
- 827-840 p. digital
Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
1432-0533
10.1007/s00401-016-1623-4 doi
Amyloid--genetics Amyotrophic Lateral Sclerosis--diagnosis Analysis of Variance Animals Bacterial Proteins--genetics Disease Models, Animal Humans In Vitro Techniques Luminescent Proteins--genetics Mice Mice, Transgenic Microscopy, Electron Mutation--genetics Organ Culture Techniques Protein Folding Proteostasis Deficiencies--diagnosis Spinal Cord--metabolism Superoxide Dismutase-1--genetics