TY - GEN AU - Gallego-Villar,L AU - Rivera-Barahona,A AU - Cuevas-Martín,C AU - Guenzel,A AU - Pérez,B AU - Barry,M A AU - Murphy,M P AU - Logan,A AU - Gonzalez-Quintana,A AU - Martín,M A AU - Medina,S AU - Gil-Izquierdo,A AU - Cuezva,J M AU - Richard,E AU - Desviat,L R TI - In vivo evidence of mitochondrial dysfunction and altered redox homeostasis in a genetic mouse model of propionic acidemia: Implications for the pathophysiology of this disorder SN - 1873-4596 PY - 2018///0109 KW - Animals KW - Antioxidants KW - metabolism KW - DNA, Mitochondrial KW - genetics KW - Disease Models, Animal KW - Homeostasis KW - Humans KW - Hydrogen Peroxide KW - Lipid Peroxidation KW - Methylmalonyl-CoA Decarboxylase KW - Mice KW - Mitochondria KW - Oxidation-Reduction KW - Oxidative Stress KW - Propionic Acidemia KW - Protein Array Analysis KW - Reactive Oxygen Species KW - Superoxides N1 - Publication Type: Journal Article UR - https://doi.org/10.1016/j.freeradbiomed.2016.04.007 ER -