Gallego-Villar, L <br/><br/>
In vivo evidence of mitochondrial dysfunction and altered redox homeostasis in a genetic mouse model of propionic acidemia: Implications for the pathophysiology of this disorder.  [electronic resource] 

 -  Free radical biology & medicine  07 2016 
 - 1-12 p.  digital 
<br/><br/> Publication Type: Journal Article 
<br/><br/><label>ISSN: </label>1873-4596 
<br/><br/><label>Standard No.: </label>10.1016/j.freeradbiomed.2016.04.007  doi 
<br/><br/><label>Subjects--Topical Terms: </label><br/>Animals<br/>Antioxidants--metabolism<br/>DNA, Mitochondrial--genetics<br/>Disease Models, Animal<br/>Homeostasis<br/>Humans<br/>Hydrogen Peroxide--metabolism<br/>Lipid Peroxidation--genetics<br/>Methylmalonyl-CoA Decarboxylase--genetics<br/>Mice<br/>Mitochondria--genetics<br/>Oxidation-Reduction<br/>Oxidative Stress--genetics<br/>Propionic Acidemia--genetics<br/>Protein Array Analysis<br/>Reactive Oxygen Species--metabolism<br/>Superoxides--metabolism