Nury, Thomas

7-Ketocholesterol is increased in the plasma of X-ALD patients and induces peroxisomal modifications in microglial cells: Potential roles of 7-ketocholesterol in the pathophysiology of X-ALD. [electronic resource] - The Journal of steroid biochemistry and molecular biology 05 2017 - 123-136 p. digital

Publication Type: Journal Article

1879-1220

10.1016/j.jsbmb.2016.03.037 doi


ATP-Binding Cassette Transporters--blood
Acyl-CoA Oxidase--blood
Adolescent
Adrenoleukodystrophy--blood
Adult
Animals
Apoptosis
Brain--pathology
Case-Control Studies
Catalase--metabolism
Cell Survival
Child
Disease Progression
Docosahexaenoic Acids--chemistry
Glutathione--chemistry
Humans
Hydrogen Peroxide--chemistry
Ketocholesterols--blood
Linoleic Acid--chemistry
Male
Membrane Proteins--blood
Mice
Microglia--cytology
Middle Aged
Oxidative Stress
Peroxisomes--metabolism
Reactive Oxygen Species--metabolism
Repressor Proteins--blood
Young Adult
alpha-Tocopherol--chemistry