Circadian profiling in two mouse models of lysosomal storage disorders; Niemann Pick type-C and Sandhoff disease. [electronic resource]
- Behavioural brain research Jan 2016
- 213-23 p. digital
Publication Type: Comparative Study; Journal Article; Research Support, Non-U.S. Gov't
1872-7549
10.1016/j.bbr.2015.10.021 doi
Actigraphy Animals CLOCK Proteins--metabolism Cholesterol--metabolism Circadian Rhythm--physiology Disease Models, Animal Fluorescent Antibody Technique Intracellular Signaling Peptides and Proteins Mice, Inbred BALB C Mice, Knockout Motor Activity--physiology Niemann-Pick C1 Protein Niemann-Pick Disease, Type C--pathology Photoperiod Proteins--genetics Retina--metabolism Rod Opsins--metabolism Sandhoff Disease--pathology Suprachiasmatic Nucleus--pathology Transcription Factor Brn-3A--metabolism beta-N-Acetylhexosaminidases--genetics