TY - GEN AU - Stepp,Susan E AU - Dufourcq-Lagelouse,Rémi AU - Kumar,Vinay TI - Pillars article: Perforin gene defects in familial hemophagocytic lymphohistiocytosis. Science. 1999. 286: 1957-1959 SN - 1550-6606 PY - 2015///0817 KW - Chromosomes, Human, Pair 10 KW - genetics KW - Cytotoxicity, Immunologic KW - History, 20th Century KW - Humans KW - Lymphocyte Activation KW - immunology KW - Lymphohistiocytosis, Hemophagocytic KW - Macrophages KW - Perforin KW - T-Lymphocytes, Cytotoxic KW - chemistry N1 - Publication Type: Biography; Classical Article; Historical Article; Journal Article ER -