TY - GEN AU - Martins,Carla AU - Hůlková,Helena AU - Dridi,Larbi AU - Dormoy-Raclet,Virginie AU - Grigoryeva,Lubov AU - Choi,Yoo AU - Langford-Smith,Alexander AU - Wilkinson,Fiona L AU - Ohmi,Kazuhiro AU - DiCristo,Graziella AU - Hamel,Edith AU - Ausseil,Jerôme AU - Cheillan,David AU - Moreau,Alain AU - Svobodová,Eva AU - Hájková,Zuzana AU - Tesařová,Markéta AU - Hansíková,Hana AU - Bigger,Brian W AU - Hrebícek,Martin AU - Pshezhetsky,Alexey V TI - Neuroinflammation, mitochondrial defects and neurodegeneration in mucopolysaccharidosis III type C mouse model SN - 1460-2156 PY - 2015///0323 KW - Acetyltransferases KW - deficiency KW - Animals KW - Behavior, Animal KW - Energy Metabolism KW - physiology KW - Gangliosides KW - metabolism KW - Glycosaminoglycans KW - Mice KW - Mice, Inbred C57BL KW - Microtubule-Associated Proteins KW - Mitochondrial Diseases KW - etiology KW - Mucopolysaccharidosis III KW - complications KW - Neuritis KW - Neurodegenerative Diseases KW - Neurologic Examination KW - Proteostasis Deficiencies KW - pathology N1 - Publication Type: Journal Article; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1093/brain/awu355 ER -