Martins, Carla

Neuroinflammation, mitochondrial defects and neurodegeneration in mucopolysaccharidosis III type C mouse model. [electronic resource] - Brain : a journal of neurology Feb 2015 - 336-55 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1460-2156

10.1093/brain/awu355 doi


Acetyltransferases--deficiency
Animals
Behavior, Animal
Energy Metabolism--physiology
Gangliosides--metabolism
Glycosaminoglycans--metabolism
Mice
Mice, Inbred C57BL
Microtubule-Associated Proteins--metabolism
Mitochondrial Diseases--etiology
Mucopolysaccharidosis III--complications
Neuritis--etiology
Neurodegenerative Diseases--etiology
Neurologic Examination
Proteostasis Deficiencies--pathology