TY  - GEN
AU  - De Stefano,Daniela
AU  - Villella,Valeria R
AU  - Esposito,Speranza
AU  - Tosco,Antonella
AU  - Sepe,Angela
AU  - De Gregorio,Fabiola
AU  - Salvadori,Laura
AU  - Grassia,Rosa
AU  - Leone,Carlo A
AU  - De Rosa,Giuseppe
AU  - Maiuri,Maria C
AU  - Pettoello-Mantovani,Massimo
AU  - Guido,Stefano
AU  - Bossi,Anna
AU  - Zolin,Anna
AU  - Venerando,Andrea
AU  - Pinna,Lorenzo A
AU  - Mehta,Anil
AU  - Bona,Gianni
AU  - Kroemer,Guido
AU  - Maiuri,Luigi
AU  - Raia,Valeria
TI  - Restoration of CFTR function in patients with cystic fibrosis carrying the F508del-CFTR mutation
SN  - 1554-8635
PY  - 2015///0914
KW  - Adaptor Proteins, Signal Transducing
KW  - metabolism
KW  - Administration, Oral
KW  - Adolescent
KW  - Adult
KW  - Animals
KW  - Apoptosis Regulatory Proteins
KW  - Beclin-1
KW  - Catechin
KW  - analogs & derivatives
KW  - Cell Membrane
KW  - Child
KW  - Chlorides
KW  - chemistry
KW  - Cystamine
KW  - pharmacology
KW  - Cysteamine
KW  - administration & dosage
KW  - Cystic Fibrosis
KW  - Cystic Fibrosis Transmembrane Conductance Regulator
KW  - genetics
KW  - Female
KW  - Homozygote
KW  - Humans
KW  - Interleukin-8
KW  - Male
KW  - Membrane Proteins
KW  - Mice
KW  - Mice, Inbred CFTR
KW  - Mice, Transgenic
KW  - Mutation
KW  - Phenotype
KW  - Pilot Projects
KW  - Sequestosome-1 Protein
KW  - Tumor Necrosis Factor-alpha
KW  - Young Adult
N1  - Publication Type: Clinical Trial, Phase II; Journal Article; Research Support, Non-U.S. Gov't
UR  - https://doi.org/10.4161/15548627.2014.973737
ER  -