De Stefano, Daniela <br/><br/>
Restoration of CFTR function in patients with cystic fibrosis carrying the F508del-CFTR mutation.  [electronic resource] 

 -  Autophagy  2014 
 - 2053-74 p.  digital 
<br/><br/> Publication Type: Clinical Trial, Phase II; Journal Article; Research Support, Non-U.S. Gov't 
<br/><br/><label>ISSN: </label>1554-8635 
<br/><br/><label>Standard No.: </label>10.4161/15548627.2014.973737  doi 
<br/><br/><label>Subjects--Topical Terms: </label><br/>Adaptor Proteins, Signal Transducing--metabolism<br/>Administration, Oral<br/>Adolescent<br/>Adult<br/>Animals<br/>Apoptosis Regulatory Proteins--metabolism<br/>Beclin-1<br/>Catechin--analogs & derivatives<br/>Cell Membrane--metabolism<br/>Child<br/>Chlorides--chemistry<br/>Cystamine--pharmacology<br/>Cysteamine--administration & dosage<br/>Cystic Fibrosis--metabolism<br/>Cystic Fibrosis Transmembrane Conductance Regulator--genetics<br/>Female<br/>Homozygote<br/>Humans<br/>Interleukin-8--metabolism<br/>Male<br/>Membrane Proteins--metabolism<br/>Mice<br/>Mice, Inbred CFTR<br/>Mice, Transgenic<br/>Mutation<br/>Phenotype<br/>Pilot Projects<br/>Sequestosome-1 Protein<br/>Tumor Necrosis Factor-alpha--metabolism<br/>Young Adult