TY - GEN AU - Noack,Julia AU - Brambilla Pisoni,Giorgia AU - Molinari,Maurizio TI - Proteostasis: bad news and good news from the endoplasmic reticulum SN - 1424-3997 PY - 2015///0511 KW - Activating Transcription Factor 6 KW - metabolism KW - Cystic Fibrosis KW - genetics KW - Endoplasmic Reticulum KW - Endoplasmic Reticulum Stress KW - Endoribonucleases KW - Enzyme Replacement Therapy KW - Eukaryotic Initiation Factor-2 KW - Hemophilia A KW - Humans KW - Lysosomal Storage Diseases, Nervous System KW - Molecular Chaperones KW - therapeutic use KW - Neurodegenerative Diseases KW - Protein Folding KW - Protein Serine-Threonine Kinases KW - Proteostasis Deficiencies KW - Signal Transduction KW - Unfolded Protein Response KW - drug effects KW - eIF-2 Kinase N1 - Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Review UR - https://doi.org/10.4414/smw.2014.14001 ER -