TY  - GEN
AU  - Harris,R A
AU  - Zhang,B
AU  - Goodwin,G W
AU  - Kuntz,M J
AU  - Shimomura,Y
AU  - Rougraff,P
AU  - Dexter,P
AU  - Zhao,Y
AU  - Gibson,R
AU  - Crabb,D W
TI  - Regulation of the branched-chain alpha-ketoacid dehydrogenase and elucidation of a molecular basis for maple syrup urine disease
SN  - 0065-2571
PY  - 1990///1026
KW  - 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)
KW  - Animals
KW  - Base Sequence
KW  - Cells, Cultured
KW  - Cloning, Molecular
KW  - DNA
KW  - genetics
KW  - Dietary Proteins
KW  - Disease Models, Animal
KW  - Homeostasis
KW  - Humans
KW  - Ketone Oxidoreductases
KW  - Kinetics
KW  - Liver
KW  - enzymology
KW  - Macromolecular Substances
KW  - Male
KW  - Maple Syrup Urine Disease
KW  - Molecular Sequence Data
KW  - Multienzyme Complexes
KW  - Oligonucleotide Probes
KW  - Rats
KW  - Rats, Inbred Strains
N1  - Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S
UR  - https://doi.org/10.1016/0065-2571(90)90021-s
ER  -