Pascual, Juan M

Triheptanoin for glucose transporter type I deficiency (G1D): modulation of human ictogenesis, cerebral metabolic rate, and cognitive indices by a food supplement. [electronic resource] - JAMA neurology Oct 2014 - 1255-65 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

2168-6157

10.1001/jamaneurol.2014.1584 doi


Adolescent
Adult
Blood Glucose--metabolism
Brain--metabolism
Carbohydrate Metabolism, Inborn Errors--drug therapy
Child
Child, Preschool
Citric Acid Cycle
Cohort Studies
Dietary Supplements
Electroencephalography
Female
Glucose--metabolism
Humans
Magnetic Resonance Imaging
Male
Monosaccharide Transport Proteins--deficiency
Treatment Outcome
Triglycerides--therapeutic use
Young Adult