TY - GEN AU - Zulian,Alessandra AU - Rizzo,Erika AU - Schiavone,Marco AU - Palma,Elena AU - Tagliavini,Francesca AU - Blaauw,Bert AU - Merlini,Luciano AU - Maraldi,Nadir Mario AU - Sabatelli,Patrizia AU - Braghetta,Paola AU - Bonaldo,Paolo AU - Argenton,Francesco AU - Bernardi,Paolo TI - NIM811, a cyclophilin inhibitor without immunosuppressive activity, is beneficial in collagen VI congenital muscular dystrophy models SN - 1460-2083 PY - 2015///0603 KW - Animals KW - Apoptosis KW - drug effects KW - Cells, Cultured KW - Collagen Type VI KW - genetics KW - Cyclosporine KW - administration & dosage KW - Disease Models, Animal KW - Humans KW - Mice KW - Mitochondria KW - metabolism KW - Muscle Strength KW - Muscular Dystrophies KW - congenital KW - Zebrafish KW - Zebrafish Proteins N1 - Publication Type: Journal Article; Research Support, Non-U.S. Gov't UR - https://doi.org/10.1093/hmg/ddu254 ER -