Zamiri, Bita

TMPyP4 porphyrin distorts RNA G-quadruplex structures of the disease-associated r(GGGGCC)n repeat of the C9orf72 gene and blocks interaction of RNA-binding proteins. [electronic resource] - The Journal of biological chemistry Feb 2014 - 4653-9 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1083-351X

10.1074/jbc.C113.502336 doi


Amyotrophic Lateral Sclerosis--genetics
Base Sequence
C9orf72 Protein
DNA Repeat Expansion--genetics
Frontotemporal Dementia--genetics
G-Quadruplexes--drug effects
Heterogeneous Nuclear Ribonucleoprotein A1
Heterogeneous-Nuclear Ribonucleoprotein Group A-B--metabolism
Humans
Nuclear Proteins--metabolism
Porphyrins--chemistry
Protein Binding--drug effects
Proteins--genetics
RNA-Binding Proteins--metabolism
Serine-Arginine Splicing Factors