Weber, Franziska D

X-linked adrenoleukodystrophy: very long-chain fatty acid metabolism is severely impaired in monocytes but not in lymphocytes. [electronic resource] - Human molecular genetics May 2014 - 2542-50 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1460-2083

10.1093/hmg/ddt645 doi


ATP Binding Cassette Transporter, Subfamily D
ATP Binding Cassette Transporter, Subfamily D, Member 1
ATP-Binding Cassette Transporters--genetics
Adrenoleukodystrophy--genetics
Adult
Case-Control Studies
Cells, Cultured
Fatty Acids--metabolism
Gene Expression
Humans
Lipid Metabolism
Lymphocytes--metabolism
Male
Middle Aged
Monocytes--metabolism
Oxidation-Reduction
Peroxisomes--metabolism