X-linked adrenoleukodystrophy: very long-chain fatty acid metabolism is severely impaired in monocytes but not in lymphocytes. [electronic resource]
- Human molecular genetics May 2014
- 2542-50 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
1460-2083
10.1093/hmg/ddt645 doi
ATP Binding Cassette Transporter, Subfamily D ATP Binding Cassette Transporter, Subfamily D, Member 1 ATP-Binding Cassette Transporters--genetics Adrenoleukodystrophy--genetics Adult Case-Control Studies Cells, Cultured Fatty Acids--metabolism Gene Expression Humans Lipid Metabolism Lymphocytes--metabolism Male Middle Aged Monocytes--metabolism Oxidation-Reduction Peroxisomes--metabolism