Pieri, Myrtani

Evidence for activation of the unfolded protein response in collagen IV nephropathies. [electronic resource] - Journal of the American Society of Nephrology : JASN Feb 2014 - 260-75 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1533-3450

10.1681/ASN.2012121217 doi


Animals
Autoantigens--genetics
Biopsy
Cells, Cultured
Collagen Type IV--deficiency
DNA-Binding Proteins--metabolism
Disease Models, Animal
Endoplasmic Reticulum Chaperone BiP
Endoplasmic Reticulum Stress--physiology
Gene Expression Profiling
Gene Knock-In Techniques
Glomerular Basement Membrane--metabolism
Heat-Shock Proteins--biosynthesis
Heterozygote
Humans
Kidney--metabolism
Mice
Mutation, Missense
Nephritis, Hereditary--genetics
Oligonucleotide Array Sequence Analysis
Podocytes--metabolism
Point Mutation
Protein Array Analysis
Protein Transport
RNA Interference
RNA, Small Interfering--pharmacology
Recombinant Fusion Proteins
Regulatory Factor X Transcription Factors
Transcription Factors--metabolism
Transfection
Unfolded Protein Response--physiology