Evidence for activation of the unfolded protein response in collagen IV nephropathies. [electronic resource]
- Journal of the American Society of Nephrology : JASN Feb 2014
- 260-75 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
1533-3450
10.1681/ASN.2012121217 doi
Animals Autoantigens--genetics Biopsy Cells, Cultured Collagen Type IV--deficiency DNA-Binding Proteins--metabolism Disease Models, Animal Endoplasmic Reticulum Chaperone BiP Endoplasmic Reticulum Stress--physiology Gene Expression Profiling Gene Knock-In Techniques Glomerular Basement Membrane--metabolism Heat-Shock Proteins--biosynthesis Heterozygote Humans Kidney--metabolism Mice Mutation, Missense Nephritis, Hereditary--genetics Oligonucleotide Array Sequence Analysis Podocytes--metabolism Point Mutation Protein Array Analysis Protein Transport RNA Interference RNA, Small Interfering--pharmacology Recombinant Fusion Proteins Regulatory Factor X Transcription Factors Transcription Factors--metabolism Transfection Unfolded Protein Response--physiology