Wu, Fenfen

Beneficial effects of bumetanide in a CaV1.1-R528H mouse model of hypokalaemic periodic paralysis. [electronic resource] - Brain : a journal of neurology Dec 2013 - 3766-74 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1460-2156

10.1093/brain/awt280 doi


Acetazolamide--pharmacology
Animals
Arginine--genetics
Bumetanide--therapeutic use
Calcium Channels, L-Type--genetics
Carbonic Anhydrase Inhibitors--pharmacology
Disease Models, Animal
Evoked Potentials, Motor--drug effects
Furosemide--pharmacology
Glucose--metabolism
Histidine--genetics
Hypokalemic Periodic Paralysis--drug therapy
In Vitro Techniques
Isometric Contraction--drug effects
Male
Mice
Mice, Transgenic
Muscle, Skeletal--physiopathology
Mutation--genetics
Sodium Potassium Chloride Symporter Inhibitors--therapeutic use