TY  - GEN
AU  - Huang,Michael Li-Hsuan
AU  - Sivagurunathan,Sutharshani
AU  - Ting,Samantha
AU  - Jansson,Patric J
AU  - Austin,Christopher J D
AU  - Kelly,Matthew
AU  - Semsarian,Christopher
AU  - Zhang,Daohai
AU  - Richardson,Des R
TI  - Molecular and functional alterations in a mouse cardiac model of Friedreich ataxia: activation of the integrated stress response, eIF2α phosphorylation, and the induction of downstream targets
SN  - 1525-2191
PY  - 2014///0312
KW  - Activating Transcription Factor 4
KW  - metabolism
KW  - Amino Acids
KW  - biosynthesis
KW  - Animals
KW  - Apoptosis
KW  - Autophagy
KW  - Cardiomegaly
KW  - pathology
KW  - Disease Models, Animal
KW  - Eukaryotic Initiation Factor-2
KW  - Female
KW  - Friedreich Ataxia
KW  - diagnostic imaging
KW  - Gene Expression Profiling
KW  - Heart Function Tests
KW  - Humans
KW  - Iron-Binding Proteins
KW  - Male
KW  - Mice
KW  - Mice, Knockout
KW  - Models, Biological
KW  - Myocardium
KW  - Myocytes, Cardiac
KW  - enzymology
KW  - Phenotype
KW  - Phosphorylation
KW  - Protein Kinases
KW  - Signal Transduction
KW  - genetics
KW  - Stress, Physiological
KW  - Ultrasonography
KW  - Frataxin
N1  - Publication Type: Journal Article; Research Support, Non-U.S. Gov't
UR  - https://doi.org/10.1016/j.ajpath.2013.05.032
ER  -