Huang, Michael Li-Hsuan

Molecular and functional alterations in a mouse cardiac model of Friedreich ataxia: activation of the integrated stress response, eIF2α phosphorylation, and the induction of downstream targets. [electronic resource] - The American journal of pathology Sep 2013 - 745-57 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1525-2191

10.1016/j.ajpath.2013.05.032 doi


Activating Transcription Factor 4--metabolism
Amino Acids--biosynthesis
Animals
Apoptosis
Autophagy
Cardiomegaly--pathology
Disease Models, Animal
Eukaryotic Initiation Factor-2--metabolism
Female
Friedreich Ataxia--diagnostic imaging
Gene Expression Profiling
Heart Function Tests
Humans
Iron-Binding Proteins--metabolism
Male
Mice
Mice, Knockout
Models, Biological
Myocardium--metabolism
Myocytes, Cardiac--enzymology
Phenotype
Phosphorylation
Protein Kinases--metabolism
Signal Transduction--genetics
Stress, Physiological--genetics
Ultrasonography
Frataxin