TY - GEN AU - Hebestreit,Helge AU - Sauer-Heilborn,Annette AU - Fischer,Rainald AU - Käding,Manfred AU - Mainz,Jochen G TI - Effects of ivacaftor on severely ill patients with cystic fibrosis carrying a G551D mutation SN - 1873-5010 PY - 2014///0929 KW - Adult KW - Aminophenols KW - administration & dosage KW - Anti-Bacterial Agents KW - Bronchi KW - metabolism KW - Cystic Fibrosis KW - drug therapy KW - Female KW - Forced Expiratory Volume KW - drug effects KW - Humans KW - Male KW - Pregnancy KW - Pregnancy Complications KW - Quinolones KW - Retrospective Studies KW - Treatment Outcome KW - Young Adult N1 - Publication Type: Journal Article; Multicenter Study UR - https://doi.org/10.1016/j.jcf.2013.05.006 ER -