Chen, Shoujun

Intracellularly-retained decorin lacking the C-terminal ear repeat causes ER stress: a cell-based etiological mechanism for congenital stromal corneal dystrophy. [electronic resource] - The American journal of pathology Jul 2013 - 247-56 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural

1525-2191

10.1016/j.ajpath.2013.04.001 doi


Animals
Corneal Dystrophies, Hereditary--genetics
Decorin--genetics
Endoplasmic Reticulum--physiology
Fluorescent Antibody Technique
Genetic Markers
HEK293 Cells
Humans
Immunoblotting
Mice
Mice, Transgenic
Microscopy, Confocal
Microscopy, Electron, Transmission
Point Mutation
Polymerase Chain Reaction
Protein Transport
Stress, Physiological
Terminal Repeat Sequences